FUNCTION: STRAIGHT-CHAIN ENOYL-COA THIOESTERS FROM C4 UP TO AT LEAST C16 ARE PROCESSED, ALTHOUGH WITH DECREASING CATALYTIC RATE. * CATALYTIC ACTIVITY: (3S)-3-hydroxyacyl-CoA = trans-2(or 3)-enoyl-CoA + H2O. * PATHWAY: SECOND STEP IN THE MITOCHONDRIAL FATTY ACID BETA-OXIDATION PATHWAY. * SUBUNIT: HOMOHEXAMER; DIMER OF TRIMERS (BY SIMILARITY). * SUBCELLULAR LOCATION: Mitochondrial matrix. * TISSUE SPECIFICITY: LIVER, FIBROBLAST, MUSCLE. BARELY DETECTABLE IN SPLEEN AND KIDNEY. * SIMILARITY: BELONGS TO THE ENOYL-COA HYDRATASE/ISOMERASE FAMILY. |
|
08-SEP-00
Last Update 13-Mar-03